Impairment of mycobacterial immunity in human interleukin-12 receptor deficiency.

Altare, F; Durandy, A; Lammas, D; Emile, J F; Lamhamedi, S; Le Deist, F; Drysdale, P; Jouanguy, E et al. · Science · 1998

basic_science · Level V

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Abstract

In humans, interferon gamma (IFN-gamma) receptor deficiency leads to a predisposition to mycobacterial infections and impairs the formation of mature granulomas. Interleukin-12 (IL-12) receptor deficiency was found in otherwise healthy individuals with mycobacterial infections. Mature granulomas were seen, surrounded by T cells and centered with epithelioid and multinucleated giant cells, yet reduced IFN-gamma concentrations were found to be secreted by activated natural killer and T cells. Thus, IL-12-dependent IFN-gamma secretion in humans seems essential in the control of mycobacterial infections, despite the formation of mature granulomas due to IL-12-independent IFN-gamma secretion.

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