Mitochondrial DNA depletion in a patient with long survival.

Vu, T H; Tanji, K; Valsamis, H; DiMauro, S; Bonilla, E · Neurology · 1998

case_report · Level V

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Abstract

We studied a 29-year-old woman with myopathy since childhood with evidence of mitochondrial DNA (mtDNA) depletion. Muscle biopsy sample showed cytochrome c oxidase (COX)-negative fibers. Biochemistry showed COX deficiency. Southern blot analysis showed 76% depletion of mtDNA as compared with controls. This patient's clinical course suggests that long survival is possible in some patients with mtDNA depletion.

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